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A 3-week-old infant with a 46,XY karyotype presents with female external genitalia and a salt-wasting crisis (hyponatremia, hyperkalemia, hypotension). An adrenocorticotropic hormone stimulation test shows low to absent levels of all steroid hormones, including pregnenolone, cortisol, aldosterone, and androgens. An adrenal ultrasound shows massively enlarged adrenal glands. What is the most likely diagnosis?

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